These are the two criteria used to determine whether your Hypermobility Spectrum Disorder (HSD) is benign, or not dangerous nor serious.
Major Criteria:
- A Beighton score of 4/9 or greater (either currently or historically)
- Arthralgia (pain in a joint) for longer than 3 months in 4 or more joints
Minor Criteria:
- A Beighton score of 1, 2 or 3 out of 9
- Arthralgia for less than 3 months in one to three joints or back pain for less than 3 months, spondylosis, spondylolysis/spondylolisthesis
- Dislocation/subluxation in more than one joint, or in one joint on more than one occasion
- Less than 3 legions of soft tissue rheumatism (e.g. epicondylitis, tenosynovitis, or bursitis)
- Marfan syndrome (tall, slim, arachnodactyly) and positive Steinberg/wrist signs (forming a loop around the narrowest part of your wrist, using your thumb and little finger)
- Abnormal skin such as striae, hyperextensibility (stretchy), thin, papyraceous scarring
- Eye signs such as drooping eyelids, myopia or antimongoloid slant
- Varicose veins, hernia or uterine/rectal prolapse
Benign Hypermobility Spectrum Disorder is diagnosed if the following are present:
- Two major criteria
- One major and two minor criteria
- Four minor criteria
Two minor criteria will suffice where there is an unequivocally affected first-degree relative.
Benign Hypermobility Spectrum Disorder is excluded by presence of Marfan or Ehlers-Danlos syndromes (other than EDS Hypermobility type). Criteria Major 1 and Minor 1 are mutually exclusive as are Major 2 and Minor 2.